Maffucci’s Syndrome is a very rare form of enchondromatosis that combines multiple enchondromas in bones anywhere in the body with benign soft tissue tumors (known as hemangiomas), which are associated with blood vessels. This condition tends to appear in the hands and feet, and has a greater tendency toward malignant transformation than Ollier’s Disease.

Some form of injury or trauma to the toe results in the formation of this bony irregularity or prominence.

Maffucci’s Syndrome only requires treatment in cases where the tumors are aggressive and begin destroying bone tissue. In these cases, surgical removal is recommended.